摘要:
目的：探讨原发性肺含铁血黄素沉着症原因和治疗方法。方法：对我科发现一例特发性肺含铁血黄素沉着症病例进行临床资料的回顾分析。结果：患儿因反复咳血丝痰一年余来我院住院，CT显示肺部团片状磨玻璃影，肺泡灌洗液可见含铁血黄素巨噬细胞。长期口服激素治疗后无咳血丝痰，CT显示病变吸收。结论：儿童出现反复咯血，不管是否合并贫血，我们应该积极考虑原发性肺含铁血黄素沉着症的可能，进行早期鉴别诊断和治疗。
Abstract:
Object: The objective was to investigate the causes and treatment of idiopathic pulmonary hemosiderosis. Method: The clinical data of one child with the disease of idiopathic pulmonary hemosiderosis in our department were retrospectively analyzed. Result: The child was transferred to our department because of coughing the sputum with blood streaks repeatedly, and the CT showed the mass-like and ground-glass-like shadow of lung. We can find siderophages in the bronchoalveolar lavage fluid. After the treatment of oral corticosteroid in long term, the child hasn’t coughed the sputum with blood streaks again and the CT showed that the lesion has been absorbed. Conclusion: Whether the child is combining anemia or not, if he has hemoptysis repeatly, we should consider that he is possible to have the disease of idiopathic pulmonary hemosiderosis and have differential diagnosis and treat him early.