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围绝经期肺淋巴管平滑肌瘤病1例及临床分析A Case of Pulmonary Lymphangiomyomatosis in Perimenopausal Women
刘伟, 林财威, 王旭东
围绝经期, 肺淋巴管平滑肌瘤病, 胸腔积液, 乳糜胸, 呼吸困难Perimenopausal Women, Pulmonary Lymphangiomyomatosis, Hydrothorax, Chylothorax, Dyspnea
《Asian Case Reports in Emergency Medicine》, Vol.3 No.3, 2015-08-31
Objective: To improve awareness and attention of pulmonary lymphangiomyomatosis (PLAM) in perimenopausal women. Method: A perimenopausal woman suffered from PLAM was analyzed in our department. Result: PLAM is a rare cystic interstitial lung disease that exclusively affects women of child-bearing age. We report a case of perimenopausal female with PLAM. Conclusion: PLAM has been seen in perimenopausal woman and should be considered in patients presenting progressive exertional dyspnea, chronic non-productive cough, spontaneous pneumothorax, chy-lothorax and a plain X-ray chest which shows a hyperinflated lung with reticular or reticulonodular pattern. Lung biopsy should be considered when there is doubt about the diagnosis. The disease prognosis is poor, and currently there are no effective prevention and treatment methods.