IgG4相关性疾病一例报道
A Case Report of IgG4-Related Kidney Disease
DOI: 10.12677/acm.2025.153763, PDF,   
作者: 梁显扬, 刘 岩*:暨南大学附属广州红十字会医院肾内科,广东 广州
关键词: IgG4相关性疾病肾活检磷脂酶A2受体IgG4-Related Disease Renal Biopsy Phospholipase A2 Receptor
摘要: IgG4相关性疾病(IgG4-related kidney disease, IgG4-RD)是近些年才被认识的一种免疫相关性疾病,发病率较低,发病原因尚不十分明确。现报道一例肾脏受累且肾穿刺活检免疫荧光检查磷脂酶A2受体(PLA2R)阳性的IgG4相关性疾病的诊治过程,以加深临床同道对该病的认识并提高诊疗水平。
Abstract: IgG4-related disease (IgG4-RD) is an immune-related condition that has only been recognized in recent years. It has a relatively low incidence, and its exact cause remains unclear. This article reports the diagnosis and treatment of a case of IgG4-RD with renal involvement and positive phospholipase A2 receptor (PLA2R) by immunofluorescence in renal puncture biopsy, in order to deepen the understanding of the disease and improve the diagnosis and treatment of the clinical colleagues.
文章引用:梁显扬, 刘岩. IgG4相关性疾病一例报道[J]. 临床医学进展, 2025, 15(3): 1458-1462. https://doi.org/10.12677/acm.2025.153763

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