完全性肺静脉异位引流一期术后死亡与肺静脉梗阻的危险因素：综述
Risk Factors for Postoperative Mortality and Pulmonary Venous Obstruction Following Primary Repair of Total Anomalous Pulmonary Venous Connection: A Review
DOI: 10.12677/acm.2026.163983, PDF,   
作者: 陈明娇, 习林云, 潘征夏*：重庆医科大学附属儿童医院胸心外科，国家儿童健康与疾病临床医学研究中心，儿童发育疾病研究教育部重点实验室，儿童发育重大疾病国家国际科技合作基地，结构性出生缺陷与器官修复重建重庆市重点实验室，重庆
关键词: TAPVC；肺静脉梗阻；术后死亡；危险因素；TAPVC； PVO； Mortality； Risk Factors
摘要: 完全性肺静脉异位引流(Total Anomalous Pulmonary Venous Connection, TAPVC)是一种罕见而危重的紫绀型先天性心脏病，若未经及时手术干预，多数患儿在婴幼儿期死亡。尽管外科技术与围术期管理显著进步，术后死亡及肺静脉梗阻(Pulmonary Venous Obstruction, PVO)仍是影响预后的关键问题。本文系统综述TAPVC术后死亡及PVO的术前、术中及术后危险因素，并总结预防与管理策略，为优化临床决策提供依据。
Abstract: Total anomalous pulmonary venous connection (TAPVC) is a rare and life-threatening cyanotic congenital heart disease. Without timely surgical intervention, the majority of affected infants die during early infancy. Despite substantial advances in surgical techniques and perioperative management, postoperative mortality and pulmonary venous obstruction (PVO) remain the principal determinants of prognosis. This review systematically summarizes the preoperative, intraoperative, and postoperative risk factors associated with mortality and PVO following TAPVC repair, and outlines current strategies for prevention and management, with the aim of informing and optimizing clinical decision-making.
文章引用：陈明娇, 习林云, 潘征夏. 完全性肺静脉异位引流一期术后死亡与肺静脉梗阻的危险因素：综述[J]. 临床医学进展, 2026, 16(3): 1963-1973. https://doi.org/10.12677/acm.2026.163983

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