脾切除后乙肝肝硬化失代偿期肝性脊髓病1例
A Case of Post-Hepatitis B Cirrhosis Complicated by Hepatic Myelopathy after Splenectomy
DOI: 10.12677/ACM.2021.118550, PDF,   
作者: 南当当, 张 锦, 高荣建, 杨 瑞, 田青鸽:延安大学附属医院消化内科,陕西 延安
关键词: 肝性脊髓病肝硬化肝性脑病Hepatic Myelopathy Liver Cirrhosis Hepatic Encephalopathy
摘要: 肝性脊髓病是一种罕见的慢性肝病的神经系统并发症,以双下肢进行性无力、痉挛性瘫痪为主要特征,该病发病率低、尚无治愈方法,且临床工作者对其发病机制、诊断及治疗了解不详,故临床上较易出现误诊、漏诊。
Abstract: Hepatic myelopathy is a rare neurological complication of chronic liver disease, which is mainly characterized by progressive weakness of both lower extremities and spastic paralysis. The incidence of the disease is low and there is no cure. And clinical workers don’t know its pathogenesis, diagnosis and treatment, so it is easy to misdiagnosis and missed diagnosis.
文章引用:南当当, 张锦, 高荣建, 杨瑞, 田青鸽. 脾切除后乙肝肝硬化失代偿期肝性脊髓病1例[J]. 临床医学进展, 2021, 11(8): 3748-3752. https://doi.org/10.12677/ACM.2021.118550

参考文献

[1] Leigh, A.D. and Card, W.I. (1949) Hepato-Lenticular Degeneration: A Case Associated with Postero-Lateral Column Degeneration. Journal of Neuropathology and Experimental Neurology, 8, 338-346. [Google Scholar] [CrossRef
[2] 河北唐山工人医院内科神经病小组. 肝硬变伴发脊髓病变2例报告[J]. 新医学, 1976(2): 107-108.
[3] 杨明芝, 吴丹, 唐亮, 等. 562例肝性脊髓病的临床特征分析[J]. 临床肝胆病杂志, 2021, 37(1): 115-119.
[4] 余思邈, 张宁, 王睿林, 等. 91例肝性脊髓病临床特点分析[J]. 胃肠病学和肝病学杂志, 2016, 25(4): 432-434.
[5] 程裕德. 肝性脊髓病993例的Meta分析[J]. 实用肝脏病杂志, 2011, 14(6): 455-456.
[6] Nardone, R.H., ller, Y., Storti, M., et al. (2014) Spinal Cord Involvement in Patients with Cirrhosis. World Journal of Gastroenterology, 20, 2578-2585. [Google Scholar] [CrossRef] [PubMed]
[7] 邵娜, 杨宇, 马芮, 等. 肝性脊髓病的研究进展[J]. 中风与神经疾病杂志, 2017, 34(11): 1054-1056.
[8] 李丽, 勾春燕, 李晶滢, 等. 肝性脊髓病的诊治进展[J]. 世界华人消化杂志, 2017, 25(29): 2631-2636.
[9] 费笑非, 胡萌萌, 秦娜, 等. 24例肝性脊髓病的临床诊治体会[J]. 中风与神经疾病杂志, 2021, 38(1): 62-64.
[10] Abby, P.C., Lijesh, K. and Philip, A. (2018) Partial Splenic Artery Embolization for Severe Hepatic Myelopathy in Cirrhosis. Hepatology, 67, 1169-1171. [Google Scholar] [CrossRef] [PubMed]
[11] 陈志惠, 陈东风. 肝性脊髓病研究进展[J]. 胃肠病学和肝病学杂志, 2016, 25(7): 832-834.
[12] 陆人杰, 朱珊梅, 唐风雷, 等. 肝性脊髓病患者临床特征的相关性分析[J]. 胃肠病学和肝病学杂志, 2014, 23(4): 446-448.
[13] 任书瑶, 吕勇, 王钲钰, 等. 经颈静脉肝内门体静脉分流术后肝性脊髓病的危险因素[J]. 中华消化杂志, 2016, 36(10): 686-691.
[14] 周颖, 邵志海, 董继宏, 等. 脊髓亚急性联合变性的临床和神经电生理特征分析[J]. 中国临床医学, 2021, 28(3): 460-464.
[15] 崔丽英, 蒲传强, 樊东升, 等. 中国肌萎缩侧索硬化诊断和治疗指南[J]. 中华神经科杂志, 2012(7): 531-533.
[16] 李晓光, 刘明生, 崔丽英. 肌萎缩侧索硬化的临床分型、分期及病情评估[J]. 协和医学杂志, 2018, 9(1): 69-74.
[17] 李雪嫣, 卢利霞, 于晓辉. 获得性肝脑变性、肝性脊髓病与肝性脑病鉴别诊断分析[J]. 肝脏, 2016, 21(10): 890-892.
[18] 唐彤丹, 朱磊, 刘永华. 6例获得性肝脑变性临床特征分析[J]. 临床肝胆病杂志, 2020, 36(10): 2274-2275.
[19] Porlas, R.V., de Castillo, L.L.C. and Dioquino, C.P.C. (2018) Neurologic Wilson Disease: Case Series on a Diagnostic and Therapeutic Emergency. Dialogues in Clinical Neuroscience, 20, 341-345. [Google Scholar] [CrossRef
[20] Weissenborn, K., Tietge, U.J., Bokemeyer, M., et al. (2003) Liver Transplantation Improves Hepatic Myelopathy: Evidence by Three Cases. Gastroenterology, 124, 346-351. [Google Scholar] [CrossRef] [PubMed]