斜坡及枕骨多发纤维结构不良1例并文献复习

Multiple Fibrous Dysplasia of the Clivus and Occipital Bone: A Case Report and Literature Review

摘要: 颅骨纤维结构不良(Fibrous dysplasia, FD)又称骨纤维异常增殖症，是一类罕见的良性骨病，多发于四肢长骨、肋骨及上颌骨，其临床症状多变，多与颅骨病变位置相关。对于其治疗应结合病变特点及临床表现实行个体化方案。本文报告本院收住的1例斜坡、枕骨多发纤维结构不良并Chairi畸形病例，参考国内外文献，分析此类病例的临床表现、影像学特点、治疗方式及管理。

Abstract: Fibrous dysplasia (FD) is a rare benign bone disease. It mostly occurs in long bones of limbs, ribs and maxilla. Its clinical symptoms are changeable and mostly related to the location of skull lesions. The treatment should be individualized according to the characteristics and clinical manifestations of the disease. This paper reports a case of multiple fibrous dysplasia of clivus and occipital bone with chairi malformation in our hospital. Referring to the literature at home and abroad, this paper analyzes the clinical manifestations, imaging characteristics, treatment and management of this kind of case.