小肠淋巴管扩张症的诊治进展
Progress in Diagnosis and Treatment of Intestinal Lymphangiectasia
DOI: 10.12677/ACM.2022.123331, PDF,   
作者: 曾天天, 詹 学*：重庆医科大学附属儿童医院消化科，国家儿童健康与疾病临床医学研究中心，儿童发育疾病研究教育部重点实验室，儿科学重庆市重点实验室，重庆
关键词: 淋巴管扩张；儿童；诊断；治疗；Intestinal Lymphangiectasia； Children； Diagnosis； Treatment
摘要: 小肠淋巴管扩张症(Intestinal lymphangiectasia, IL)是由各种原因所致淋巴管内压力升高，淋巴液漏入肠腔引起的一系列临床症状。主要临床表现为水肿、腹泻、腹胀，可伴有腹水、发热、电解质紊乱等。根据典型临床表现和内镜下可见淋巴管扩张及组织病理学表现即可确诊。低脂、富含中链甘油三酯(medium-chain-triacylglycerol, MCT)的饮食为主要治疗方式。由于此病罕见，对该病的认识仍较为局限。现对小肠淋巴管扩张症的相关文献进行综述，获得该病诊治的最新进展，提高对该病的认识。
Abstract: Intestinal lymphangiectasia (IL) is a series of clinical symptoms caused by the increase of pressure in lymphatic vessels and lymphatic fluid leakage into the intestinal cavity due to various reasons. The main clinical manifestations are edema, diarrhea, abdominal distension, accompanied by ascites, fever, electrolyte disorder, etc. The diagnosis was made on the basis of typical clinical manifestations, endoscopic lymphangiectasia, and histopathological findings. A low-fat, medium-chain-triacylglycerol (MCT) diet was the primary treatment. Due to its rarity, the understanding of this disease is still limited. This paper reviews the literature on intestinal lymphangiectasia to obtain the latest progress in diagnosis and treatment of this disease and improve the understanding of this disease.
文章引用：曾天天, 詹学. 小肠淋巴管扩张症的诊治进展[J]. 临床医学进展, 2022, 12(3): 2303-2309. https://doi.org/10.12677/ACM.2022.123331

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