非酮症性糖尿病性偏身舞蹈症伴脑微出血1例
A Case of Non Ketotic Diabetes Hemichorea with Cerebral Hemorrhage
DOI: 10.12677/ACM.2022.1281132, PDF,   
作者: 温 华, 苏媛媛：西安医学院第一附属医院消化内科，陕西 西安；西安医学院，陕西 西安；路 宁, 张明鑫*：西安医学院第一附属医院消化内科，陕西 西安；曾 新, 张 洁：西安医学院，陕西 西安
关键词: 非酮症性糖尿病性偏身舞蹈症；脑微出血；磁共振成像；Non Ketotic Diabetes Hemichorea； Cerebral Microbleeds； Magnetic Resonance Imaging
摘要: 目的：报道1例非酮症性糖尿病性偏身舞蹈症伴脑微出血的诊治过程，旨在进一步提高对该类疾病的认识和处理。方法：回顾性分析2021年5月18日西安医学院第一附属医院神经内科收治的1例非酮症性糖尿病性偏身舞蹈症伴脑微出血患者的临床资料及相关文献复习。结果：患者临床表现为偏侧舞蹈样运动，伴血糖增高，MRI提示脑微出血。最终诊断为非酮症性糖尿病性偏身舞蹈症、脑微出血。经降糖和抗锥体外系治疗后患者症状明显改善。结论：非酮症性糖尿病性偏身舞蹈症是临床上比较罕见的锥体外系疾病，目前发病机制不明，临床医生需高度引起重视，以期早期识别、早期诊断及早期治疗，减少误诊漏诊。
Abstract: Objective: To report the diagnosis and treatment of a case of non ketotic diabetes hemichorea with cerebral microbleeds, in order to further improve the understanding and treatment of this kind of disease. Methods: The clinical data of a case of non ketotic diabetes hemichorea with cerebral mi-crobleeds admitted to the Department of Neurology, the First Affiliated Hospital of Xi’an Medical College on May 18, 2021 were analyzed retrospectively and the relevant literature was reviewed. Results: The clinical manifestation of the patient was laterally choreographic movement with in-creased blood glucose. MRI showed cerebral microbleeds. The final diagnosis was non ketotic dia-betes hemichorea and cerebral microbleeds. The symptoms of the patients were significantly im-proved after hypoglycemic and anti pyramidal extracorporeal therapy. Conclusion: Non ketotic di-abetes hemichorea is a relatively rare extrapyramidal disease in clinic. At present, the pathogenesis is unknown. Clinicians need to pay high attention to it in order to early identify, early diagnose and early treat, and reduce misdiagnosis and missed diagnosis.
文章引用：温华, 路宁, 曾新, 张洁, 苏媛媛, 张明鑫. 非酮症性糖尿病性偏身舞蹈症伴脑微出血1例[J]. 临床医学进展, 2022, 12(8): 7859-7864. https://doi.org/10.12677/ACM.2022.1281132

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