具有自身免疫特征的儿童间质性肺炎的1例临床分析

Clinical Analysis of 1 Case of Interstitial Pneumonia in Children with Autoimmune Features

摘要: 自身免疫特征的间质性肺炎(interstitial pneumonia with autoimmune features, IPAF)是一种临床特征提示有潜在的自身免疫性过程，但不符合既定的结缔组织病(Connective tissue disease, CTD)标准的特发性间质性肺炎(Interstitial pneumonia, IIP)。可累及血管、皮肤、关节、肺等器官，病情呈反复发作和缓解的交替过程，以女性发病率居多，大部分患者预后良好，肺部血管受累者预后不佳。现将西安市儿童医院收治的1例自身免疫特征的间质性肺炎患者临床资料及诊疗过程，结合相关文献学习，做如下报道。

Abstract: Interstitial pneumonia with autoimmune features is a clinical feature that suggests an underlying autoimmune process but does not meet the established criteria for connective tissue disease Interstitial pneumonia. It can involve blood vessels, skin, joints, lungs and other organs, and the condition is an alternating process of recurrent attacks and remission, with most female morbidity, most patients have a good prognosis, and pulmonary vascular involvement has a poor prognosis. The clinical data and diagnosis and treatment process of one patient with interstitial pneumonia with autoimmune characteristics admitted to Xi’an Children’s Hospital are combined with relevant literature study to make the following report.