川崎病休克综合征伴巨噬细胞活化综合征1例

A Case of Kawasaki Disease Shock Syndrome with Macrophage Activation Syndrome

摘要: 川崎病在儿童中较常见，是儿童时期后天性心脏病最常见的原因，川崎病休克综合征则较少见，抢救难度大，我科近期收治一例川崎病休克综合征，该患儿不仅合并多系统功能损害还有巨噬细胞活化综合征，病初明确诊断较困难，经过积极完善相关检查后明确诊断，并且从入院即予积极抢救治疗，故治疗疗效较好，患儿住院治疗15天后治愈出院。出院后随访无特殊，正常上学与生活。

Abstract: Kawasaki disease is the most common cause of acquired heart disease in childhood. Kawasaki dis-ease shock syndrome is less common and difficult to rescue. Recently, a case of Kawasaki disease shock syndrome was admitted to our department. The child was not only complicated with multiple system dysfunction, but also macrophage activation syndrome. It was difficult to make a dear diag-nosis at the beginning. After actively improving the relevant examinations, the diagnosis was made and the patient was actively rescued from admission, the treatment effect was good. The child was cured and discharged after 15 days of hospitalization. Follow-up after discharge showed no special with normal school and life.