结缔组织病合并获得性凝血因子V缺乏1例
A Case Report of Connective Tissue Disease Combined with Acquired Factor V Deficiency
DOI: 10.12677/ACM.2023.133646, PDF,   
作者: 武锐锋：延安大学附属医院风湿免疫科，陕西 延安
关键词: 凝血因子V；自身免疫性疾病；激素；Coagulation Factor V； Autoimmune Diseases； Hormones
摘要: 凝血因子V是凝血过程中必不可少的合成凝血酶原复合物的组成成分。获得性凝血因子V缺乏症是一种罕见的血液系统疾病。本文报道了1例结缔组织病合并获得性凝血因子V缺乏症患者，通过激素和免疫抑制治疗，患者凝血功能逐渐恢复，考虑发生获得凝血因子V缺乏可能与自身免疫性疾病有关。本文旨在为临床医生的诊断和治疗提供思路，综合文献分析如下。
Abstract: Coagulation factor V is a component of the synthetic prothrombin complex that is essential in the coagulation process. Acquired coagulation factor V deficiency is a rare hematologic disorder. In this paper, we report a patient with connective tissue disease combined with acquired coagulation fac-tor V deficiency, who gradually recovered coagulation function through hormonal and immunosup-pressive treatment, and consider that the occurrence of acquired coagulation factor V deficiency may be related to autoimmune diseases. The purpose of this article is to provide clinicians with ideas for diagnosis and treatment, and a comprehensive literature analysis is presented below.
文章引用：武锐锋. 结缔组织病合并获得性凝血因子V缺乏1例[J]. 临床医学进展, 2023, 13(3): 4507-4510. https://doi.org/10.12677/ACM.2023.133646

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