腹膜后、胸背部皮肤多部位不同组织学类型淋巴管瘤一例

One Case of Lymphangioma with Different Histological Types in Multiple Parts of Retroperitoneal and Thoracolumbra Skin

摘要: 目的：通过探讨胸背部皮肤、腹膜后多部位不同组织学类型淋巴管瘤的临床表现、影像学检查、病理以及诊断，探讨淋巴管瘤的治疗方法及疗效。方法：回顾性分析1例多部位不同组织学类型淋巴管瘤患者的临床资料。结果：患者通过手术治疗完整切除胸背部皮肤淋巴管瘤、腹膜后淋巴管瘤，术后恢复良好，左侧胸壁皮肤淋巴管瘤切除术后45个月左侧背部皮肤出现淋巴管瘤，再次行手术切除术后持续随访至今未复发。腹膜后淋巴管瘤随访5个月未复发。结论：同一个体多部位不同组织学类型的淋巴管瘤临床上十分罕见，术前需行全面检查，避免漏诊，术前明确诊断较困难，手术为首选治疗，切除肿瘤的完整性是降低复发率的关键。

Abstract: Objective: To investigate the clinical manifestations, imaging examination, pathology and diagnosis of different histological types of lymphangioma in thoracic and dorsal skin and retroperitoneum, and to explore the therapeutic methods and efficacy of lymphangioma. Methods: The clinical data of a patient with multiple sites and different histological types of lymphangioma were analyzed retro-spectively. Results: The patient underwent complete resection of thoracic and dorsal cutaneous lymphangioma and retroperitoneal lymphangioma, and recovered well after surgery. The left dor-sal cutaneous lymphangioma appeared 45 months after resection of the left thoracic wall cutaneous lymphangioma, and there was no recurrence until now after continuous follow-up after surgical re-section. Retroperitoneal lymphangioma was followed up for 5 months without recurrence. Conclu-sion: Lymphangioma of multiple sites and different histological types in the same individual is very rare in clinical practice. Preoperative comprehensive examination is needed to avoid missed diag-nosis, and preoperative definite diagnosis is difficult. Surgery is the preferred treatment, and the integrity of tumor resection is the key to reduce the recurrence rate.