儿童心肌致密化不全的研究进展
Research Progress of Non-Compaction of the Ventricular Myocardium in Children
DOI: 10.12677/ACM.2023.13102172, PDF,   
作者: 夏尔巴提·别克沙特：新疆医科大学儿科学院，新疆 乌鲁木齐；阿布来提·阿不都哈尔*：新疆医科大学第一附属医院小儿急危重症医学科，新疆 乌鲁木齐
关键词: 心肌致密化不全；儿童；诊断；预后；Non-Compaction of the Ventricular Myocardium； Children； Diagnosis； Prognosis
摘要: 心肌致密化不全(NVM)是一种罕见的、未分类的心肌病，临床上可表现为进行性加重的心功能不全、心律失常和血栓形成。这类心肌病的诊断是基于临床表现及各种超声心动图、心脏磁共振(CMR)等心脏成像技术共同诊断的；目前对于本病还没有足够的数据去建立可靠的治疗指南，主要是针对缓解临床症状及处理并发症。本病的预后因早期诊断、及时对症治疗及预防并发症而有明显差异。本文旨在对NVM的病因、发病机制、诊断标准、治疗及预后进行全面综述。
Abstract: Non-compaction of the ventricular myocardium (NVM) is a rare and unclassified cardiomyopathy, which can be clinically manifested as progressive heart failure, arrhythmia and thrombosis. The diagnosis of this type of cardiomyopathy is based on clinical manifestations and various cardiac im-aging techniques such as echocardiography and cardiac magnetic resonance (CMR). At present, there are not enough data to establish reliable treatment guidelines for this disease. Now its thera-pies mainly focus on relieving clinical symptoms and managing complications. The prognosis of this disease is significantly different due to early diagnosis, timely symptomatic treatment and preven-tion of complications. This article aims to comprehensively review the etiology, pathogenesis, diag-nostic criteria, treatment and prognosis of NVM.
文章引用：夏尔巴提·别克沙特, 阿布来提·阿不都哈尔. 儿童心肌致密化不全的研究进展[J]. 临床医学进展, 2023, 13(10): 15530-15536. https://doi.org/10.12677/ACM.2023.13102172

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