IRVAN综合征治疗一例及文献复习
A Case of Idiopathic Retinal Vasculitis, Aneu-rysms, and Neuroretinitis (IRVAN) Syndrome and a Literature Review
DOI: 10.12677/ACM.2023.13102212, PDF,    科研立项经费支持
作者: 李艳秋：青岛大学青岛医学院，山东 青岛；高 杰：潍坊医学院临床医学院，山东 潍坊；刘同同：锦州医学院临床医学院，辽宁 锦州；王 涛*：山东省临沂市人民医院眼科，山东 临沂
关键词: 特发性视网膜血管炎；动脉瘤；视神经视网膜炎；IRVAN综合征；Idiopathic Retinal Vasculitis； Aneurysms； Neuroretinitis； IRVAN Syndrome
摘要: 目的：报道1例特发性视网膜血管炎、动脉瘤、视神经视网膜炎(IRVAN)综合征治疗过程的临床特征和治疗要点，分析该病形成原因及治疗预后。方法：回顾该病例的诊疗过程，并结合相关文献分析该病表现及治疗预后。结果：根据患者病史、症状、体征及眼底荧光素血管造影结果，诊断为“IRVAN综合征III期”，行玻璃体腔注射及激光光凝，随访10个月，病情稳定。结论：IRVAN综合征较为罕见，如果不及早进行诊断和治疗，预后通常较差。因此，提高对该疾病的认识对于提高患者的生存质量至关重要。
Abstract: Objective: This study reports the clinical features and treatment of a case of Idiopathic Retinal Vas-culitis, Aneurysms, and Neuroretinitis (IRVAN) Syndrome and analyzes the cause and treatment prognosis of the disease. Methods: The diagnosis and treatment of this case were reviewed, and the manifestations and prognosis of this disease were analyzed combined with related literatures. Re-sults: According to the patient’s medical history, symptoms, signs and fundus fluorescein angi-ography results, we diagnosed “IRVAN Syndrome Stage III”. We successfully treated with intravi-treal injection and Laser photocoagulation. After 10 months of follow-up, the condition was stable. Conclusion: IRVAN syndrome is rare, and the prognosis is usually poor if it is not diagnosed and treated early. Therefore, it is very important to improve the understanding of the disease for im-proving the quality of life of patients.
文章引用：李艳秋, 高杰, 刘同同, 王涛. IRVAN综合征治疗一例及文献复习[J]. 临床医学进展, 2023, 13(10): 15829-15834. https://doi.org/10.12677/ACM.2023.13102212

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