胸腺瘤术后致莫旺综合征一例临床特征及文献复习
Clinical Features and Literature Review of One Case of Myxedema Coma after Thymoma Surgery
DOI: 10.12677/acm.2025.15123571, PDF,   
作者: 訾 恒：济宁医学院临床医学院，山东 济宁；张 璇*, 赵昊天：济宁市第一人民医院神经内科，山东 济宁
关键词: 莫旺综合征；血浆置换；副肿瘤综合征；Morvan Syndrome； Plasma Exchange； Paraneoplastic Syndrome
摘要: 莫旺综合征(Morvan Syndrome, MoS)是一种罕见的自身免疫性神经综合征，胸腺瘤是MoS最重要的副肿瘤性病因之一。本病例是一例典型的B2型胸腺瘤切除术后继发的MoS，在激素治疗效果不佳的情况下，及时启动血浆置换(plasma exchange, PLEX)取得了显著疗效，为临床医生认识这一罕见疾病提供了重要启示。
Abstract: Morvan syndrome (MoS) is a rare autoimmune neurological syndrome, and thymoma is one of the most important paraneoplastic causes of MoS. This case is a typical MoS that occurred after the resection of a type B2 thymoma. When hormone therapy was ineffective, timely initiation of plasma exchange (PLEX) achieved significant therapeutic effects, providing important insights for clinicians in recognizing this rare disease.
文章引用：訾恒, 张璇, 赵昊天. 胸腺瘤术后致莫旺综合征一例临床特征及文献复习[J]. 临床医学进展, 2025, 15(12): 1611-1616. https://doi.org/10.12677/acm.2025.15123571

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