腹膜后胚胎型横纹肌肉瘤1例并文献复习
Retroperitoneal Embryonal Rhabdomyosarcoma: A Case Report and Literature Review
摘要: 腹膜后胚胎型横纹肌肉瘤(eRMS)临床罕见，易侵犯周围血管。本文报道了1例10岁儿童因腹膜后eRMS包绕髂内动脉的病例，影像学检查显示腹膜后巨大混杂密度肿块，增强后边缘强化、中央坏死，数字减影血管造影(DSA)证实肿瘤血供丰富。通过术前行超选择性动脉栓塞减少术中出血，最终成功实施肿瘤切除术的一例诊疗过程。
Abstract: Retroperitoneal embryonal rhabdomyosarcoma (eRMS) is clinically rare and prone to invading surrounding vessels. This paper reports a case of a 10-year-old child with retroperitoneal eRMS encircling the internal iliac artery. Imaging revealed a large heterogeneous density mass in the retroperitoneum, demonstrating marginal enhancement and central necrosis after contrast administration. Digital subtraction angiography (DSA) confirmed abundant tumour blood supply. The diagnostic and therapeutic process is detailed, including preoperative superselective arterial embolisation to minimise intraoperative haemorrhage, culminating in successful tumour resection.
文章引用：杨永梅, 罗亮, 许俊锋. 腹膜后胚胎型横纹肌肉瘤1例并文献复习[J]. 临床医学进展, 2026, 16(1): 261-266. https://doi.org/10.12677/acm.2026.161039

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